Sclerosing Stromal Tumor of the Ovary in a three-year-old Girl

Sclerosing stromal tumor of the ovary is a rare, benign ovarian tumor, seen primarily in young women. We report a 3-year-old girl who presented with a palpable lower abdominal mass. Computed Tomography (CT) study revealed a huge pelvic mass with an enhancement pattern typical of ovarian sclerosing stromal tumor. The diagnosis was confirmed by pathology examination of the surgically resected tumor. Correspondence Author to: Shin-Lin Shih Department of Radiology, Mackay Memorial Hospital, Taipei, Taiwan No. 92, Sec. 2, Zhong-Shan N. Road, Taipei 104, Taiwan J Radiol Sci 2011; 36: 59-62 Sclerosing stromal tumor of the ovary 60 J Radiol Sci March 2011 Vol.36 No.1 this young, the imaging characteristics help to clarify the diagnosis. Primary ovarian neoplasms are classified as epithelial, germ cell, and sex cord-stromal tumors. In adults, epithelial ovarian tumors are the most common, followed by germ cell tumors, and then stromal tumors. The pathology spectrum in pediatric patients is similar to that in adults, but the frequency and clinical behavior are different. Germ cell tumors account for more than two thirds of pediatric ovarian tumors, epithelial tumors 17%, and stromal tumors 13% [4, 5]. Sex cord-stromal tumors of ovary include SST, granulosa cell tumor, fibroma-thecoma, Sertoli-Leydig cell tumor, steroid cell tumor, and others. SST accounts for only 6% sex-cord stromal tumors [4] and was first identified as a distinctive subtype within the fibroma-thecoma group